Neuromuscular DiseasesNeuromuscular DiseasesНервно-мышечные болезни2222-87212413-0443Publishing House ABV Press21410.17650/2222-8721-2017-7-3-56-62CLINICAL CASEКЛИНИЧЕСКИЙ РАЗБОРBickerstaff brainstem encephalitis, acute transverse myelitis, and acute motor axonal neuropathy: diagnostic and treatment challenges in patients with concomitant syndromes. Clinical observationСтволовой энцефалит Бикерстаффа, острый поперечный миелит и острая моторная аксональная нейропатия: сложности диагностики и лечения пациентов с перекрестными синдромами. Клиническое наблюдениеMurtazinaA. F.МуртазинаА. Ф.
Russian Federation
aysylumurtazina@gmail.comNaumovaE. S.НаумоваЕ. С.
Russian Federation
aysylumurtazina@gmail.comNikitinS. S.НикитинС. С.
Russian Federation
aysylumurtazina@gmail.comBoriskinaL. M.БорискинаЛ. М.
Russian Federation
aysylumurtazina@gmail.comLagutinA. V.ЛагутинА. В.
Russian Federation
aysylumurtazina@gmail.comMedical Center “Practical Neurology”Медицинский центр «Практическая неврология»Normodent Central ClinicООО «Нормодент Клиника центральная»Central Clinical Hospital of the Administration of the President of the Russian FederationФГБУ «Центральная клиническая больница с поликлиникой» Управления делами Президента Российской Федерации071120177356620711201707112017Copyright ©; 2017, Murtazina A.F., Naumova E.S., Nikitin S.S., Boriskina L.M., Lagutin A.V.Copyright ©; 2017, Муртазина А.Ф., Наумова Е.С., Никитин С.С., Борискина Л.М., Лагутин А.В.2017Murtazina A.F., Naumova E.S., Nikitin S.S., Boriskina L.M., Lagutin A.V.Муртазина А.Ф., Наумова Е.С., Никитин С.С., Борискина Л.М., Лагутин А.В.https://creativecommons.org/licenses/by/4.0https://nmb.abvpress.ru/jour/article/view/214

We report a 40-year-old woman presented with consciousness disturbance, ataxia, asymmetrical limb weakness, hyperreflexia. Due to magnetic resonance imaging findings, the patient was diagnosed with Bickerstaff’s brainstem encephalitis overlapped with acute transverse myelitis. Later she developed distal muscles atrophy and the electroneuromyographic study revealed axonal motor neuropathy, therefore acute motor axonal neuropathy was diagnosed. The patient underwent one course of intravenous immunoglobulin therapy with the regression of symptoms and magnetic resonance imaging changes. Nine months after symptoms onset, the patient has completely recovered. This overlapping case of Bickerstaff’s brainstem encephalitis, acute transverse myelitis and acute motor axonal neuropathy provides further support that these conditions are part of the same spectrum.

 

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