Neuromuscular DiseasesNeuromuscular DiseasesНервно-мышечные болезни2222-87212413-0443Publishing House ABV Press47310.17650/2222-8721-2022-12-1-21-28LECTURES AND REVIEWSЛЕКЦИИ И ОБЗОРЫPossibilities of ultrasound in the diagnosis and differential diagnosis of amyotrophic lateral sclerosis: a literature reviewВозможности ультразвукового исследования в диагностике и дифференциальной диагностике бокового амиотрофического склероза: обзор литературыhttps://orcid.org/0000-0003-4547-1263MansurovaA. V.МансуроваА. В.
Russian Federation

Anna Victorovna Mansurova

80 Volokolamskoe shosse, Moscow 125367

Анна Викторовна Мансурова

Москва 125367, Волоколамское шоссе, 80

anyneurology@mail.ruhttps://orcid.org/0000-0002-8726-8928ChechetkinA. O.ЧечёткинА. О.
Russian Federation

80 Volokolamskoe shosse, Moscow 125367

Москва 125367, Волоколамское шоссе, 80

https://orcid.org/0000-0003-3956-6362SuponevaN. A.СупоневаН. А.
Russian Federation

80 Volokolamskoe shosse, Moscow 125367

Москва 125367, Волоколамское шоссе, 80

https://orcid.org/0000-0002-1072-9968ZakharovaM. N.ЗахароваМ. Н.
Russian Federation

80 Volokolamskoe shosse, Moscow 125367

Москва 125367, Волоколамское шоссе, 80

https://orcid.org/0000-0002-7924-3405GrishinaD. A.ГришинаД. А.
Russian Federation

80 Volokolamskoe shosse, Moscow 125367

Москва 125367, Волоколамское шоссе, 80

Research Center of NeurologyФГБНУ «Научный центр неврологии»1402202212121281402202214022022Copyright ©; 2022, Mansurova A.V., Chechetkin A.O., Suponeva N.A., Zakharova M.N., Grishina D.A.Copyright ©; 2022, Мансурова А.В., Чечёткин А.О., Супонева Н.А., Захарова М.Н., Гришина Д.А.2022Mansurova A.V., Chechetkin A.O., Suponeva N.A., Zakharova M.N., Grishina D.A.Мансурова А.В., Чечёткин А.О., Супонева Н.А., Захарова М.Н., Гришина Д.А.https://creativecommons.org/licenses/by/4.0https://nmb.abvpress.ru/jour/article/view/473

Amyotrophic lateral sclerosis is a neurodegenerative disease with a steady and rapid progression, manifested, in addition to the loss of strength of the muscles of the limbs and trunk, the development of fatal bulbar and respiratory disorders. Due to the need for early detection of this pathology, a large number of diagnostic tests have been proposed, which make it possible to suspect a motor neuron disease in a patient with a high probability. However, due to the polymorphic clinical picture of the disease, currently there are diagnostic situations in which existing methods do not allow to establish a reliable diagnosis or it becomes possible only at the later stages of the disease. This review examines the modern possibilities of ultrasound examination of peripheral nerves and muscles in the diagnosis and differential diagnosis of amyotrophic lateral sclerosis.

Боковой амиотрофический склероз является нейродегенеративным заболеванием с неуклонным и быстрым прогрессированием, проявляющимся, помимо утраты силы мышц конечностей и туловища, развитием фатальных бульбарных и дыхательных нарушений. В связи с необходимостью раннего выявления данной патологии было предложено большое количество диагностических тестов, позволяющих с высокой вероятностью заподозрить у пациента болезнь двигательного нейрона. Однако в связи с полиморфной клинической картиной заболевания в настоящее время остаются диагностические ситуации, при которых существующие методики не позволяют установить достоверный диагноз или позволяют это сделать лишь на поздних этапах заболевания. В данном обзоре рассматриваются современные возможности ультразвукового исследования периферических нервов и мышц в диагностике и дифференциальной диагностике бокового амиотрофического склероза.

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