Email this article Clinical case of the late diagnosis of neurolipomatosis (Dercum’s disease)
- Authors: Shnayder N.A.1, Kiselev I.A.2, Dmitrenko D.V.2
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Affiliations:
- Prof. V.F. Voino-Yasenetsky Krasnoyarsk State Medical University, Ministry of Health of the Russian Federation Clinical Hospital Fifty-One, Federal Biomedical Agency of Russia, Zheleznogorsk
- Prof. V.F. Voino-Yasenetsky Krasnoyarsk State Medical University, Ministry of Health of the Russian Federation
- Issue: Vol 3, No 2 (2013)
- Pages: 45-52
- Section: CLINICAL DISCUSSION
- Published: 20.06.2013
- URL: https://nmb.abvpress.ru/jour/article/view/49
- DOI: https://doi.org/10.17650/2222-8721-2013-0-2-
- ID: 49
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Abstract
Dercum’s disease (Dercum’s syndrome, neurolipomatosis) is a rare and inadequately studied chronic disease that is characterized by subcutaneous fatty deposits in different parts of the trunk and accompanied by compression-ischemic neuropathy of the cutaneous branches of peripheral nerves with pain syndrome, pathological fatigue, and obesity. The most common site of subcutaneous deposits is the upper extremities, elbows, anterior abdominal wall, buttocks, thighs, and knees. However, Dercum’s disease is systemic and can be manifested by a wide range of symptoms and it frequently recurs, including after surgical removal of lipomas. The paper presents a case of the late diagnosis of neurolipomatosis in a 23-year-old male. It considers the etiology, pathogenesis, and diagnosis of the disease and current approaches to its treatment. A better understanding of the characteristic clinical syndrome of painful lipomatosis will assist in the early diagnosis of the disease and in the prevention of inadequate therapy cases.
About the authors
N. A. Shnayder
Prof. V.F. Voino-Yasenetsky Krasnoyarsk State Medical University, Ministry of Health of the Russian FederationClinical Hospital Fifty-One, Federal Biomedical Agency of Russia, Zheleznogorsk
Author for correspondence.
Email: NASchnaider@yandex.ru
Russian Federation
I. A. Kiselev
Prof. V.F. Voino-Yasenetsky Krasnoyarsk State Medical University, Ministry of Health of the Russian Federation
Email: fake@neicon.ru
Russian Federation
D. V. Dmitrenko
Prof. V.F. Voino-Yasenetsky Krasnoyarsk State Medical University, Ministry of Health of the Russian Federation
Email: fake@neicon.ru
Russian Federation
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